Question: What Organs Are Primarily Affected By Cystic Fibrosis?

How old is the oldest person with cystic fibrosis?

Senior citizens with cystic fibrosis The oldest person diagnosed with CF for the first time in the U.S.

was 82, in Ireland was 76, and in the United Kingdom was 79..

What is cystic fibrosis life expectancy?

Outlook (Prognosis) Many young adults with CF finish college or find jobs. Lung disease eventually worsens to the point where the person is disabled. Today, the average life span for people with CF who live to adulthood is about 44 years. Death is most often caused by lung complications.

Can you get cystic fibrosis later in life?

While cystic fibrosis is usually diagnosed in childhood, adults with no symptoms (or mild symptoms) during their youth can still be found to have the disease.

Does cystic fibrosis affect the digestive system?

About 90 percent of people with CF have sticky mucus that blocks ducts in the pancreas and prevents enzymes from reaching the small intestine to digest food. Undigested food in the intestines can cause pain, cramping, gas and either loose, greasy, floating stools or constipation and blockages.

Does cystic fibrosis affect the spleen?

In the literature, spontaneous splenic rupture is mostly described in association with infections, inflammatory disease or malignancy—that is, conditions in which the spleen enlarges over a short period of time—whereas no such association is reported in cystic fibrosis.

Where is cystic fibrosis most common?

The cystic fibrosis gene is most common in Caucasians of northern European descent. The disease occurs most frequently in these people, but can occur in any ethnic population.

What is the end stage of cystic fibrosis?

Common symptoms at the end of life include dyspnea, fatigue, anxiety, anorexia, pain, and cough (see Fast Facts #27, 199, 200). Care providers must balance benefit versus burden of disease-specific treatments such as nebulized medications, NIPPV, and chest physiotherapy.

How do CF patients die?

Mucus in CF patients is very thick and accumulates in the intestines and lungs. The result is malnutrition, poor growth, frequent respiratory infections, breathing difficulties, and eventually permanent lung damage. Lung disease is the usual cause of death in most patients.

Can you have cystic fibrosis without lung problems?

But new research suggests that this pulmonary view of cystic fibrosis is only half of the picture: a suite of symptoms associated with cystic fibrosis can also occur in patients who do not have lung disease at all, indicating that cystic fibrosis is really two diseases.

What do stools look like with cystic fibrosis?

Because of CF’s effects on the digestive system, a child with CF may have these symptoms: Frequent, bulky, greasy stools. A rare condition where the end part of the bowels comes out of the anus (rectal prolapse) A bowel blockage caused by a baby’s thick and sticky first bowel movement (meconium ileus)

Is there a mild form of cystic fibrosis?

Atypical CF is a milder form of the CF disorder, which is associated with mutations of the cystic fibrosis transmembrane receptor gene. Instead of having classic symptoms, individuals with atypical CF might only have mild dysfunction in 1 organ system and might or might not have elevated sweat chloride levels.

Can a woman with CF have a baby?

Most female CF patients have no problems conceiving. The thicker mucus can make it more difficult for sperm to penetrate the cervix, increasing the amount of time needed for a woman to get pregnant. Typically, pregnant moms with CF have healthy pregnancies and their babies are born just fine.

Who does cystic fibrosis affect the most?

Cystic fibrosis is the most common genetic disease in white people. It affects about 30,000 children and adults in the United States and about 70,000 people worldwide. Although cystic fibrosis is more commonly found in the white population, the disease affects all racial groups.

Can you kiss someone with cystic fibrosis?

It is logical, that germs are exchanged in both directions when kissing, so that bacteria can also be transmitted to the kissing CF patient. A healthy person without an acute infection is however no danger for transmitting germs to the CF partner. It is a special situation, if both partners suffer from CF.

What are the odds of cystic fibrosis?

About one in every 35 Americans is a symptomless carrier of the defective CFTR gene. Only about one of every 3,000 Caucasian newborns has CF. We know there are more than 1,700 mutations of the CFTR gene.